North East Thames Regional Genetics Service

Address

Regional Molecular Genetics

Great Ormond Street Hospital

Level 6, York House

37 Queen Square

London WC1N 3BH

Contact 1

 Lucy Jenkins

Contact 2

 Sam Loughlin

Contact 3

 

Telephone 1

 020 7762 6888

Telephone 2

 

Fax:

 020 7813 8196

Email 1

 Lucy.Jenkins@gosh.nhs.uk

Email 2

 LoughS@gosh.nhs.uk

Email 3

 

Home page

 http://www.ich.ucl.ac.uk/gosh/clinicalservices/Molecular_Genetics/Homepage

 

 

Services offered: 18/03/2010 update

Disease

OMIM

UKGTN service

(Approved, Pending, N/A)

 Achondroplasia (FGFR3)

 #100800

 *134934

 YES

 Albright's Hereditary Osteodystrophy (GNAS1)

 #103580

 +139320

 YES

 Aminoglycoside induced deafness (MTRNR1 – m.1555A>G)

 #580000

*561000

 

 Angelman syndrome

 #105830

 

 Apert syndrome (FGFR2)

 #101200

*176943

 NCG

 Athabaskan-type severe combined immune deficiency (SCID with sensitivity to ionizing radiation) (DCLREC1C)

 #602450

*605988

 NCG

Autoimmune lymphoproliferative syndrome (TNFRSF6)

 #601859

*134637

 NCG

 Autosomal recessive Osteopetrosis (TCIRG1)

 #259700

*604592

 YES

Beckwith-Wiedemann Syndrome

#130650

 

 Branchio-oto-renal syndrome (EYA1, SIX1, SIX5)

 #133650

*601653

 YES

 Carbamoylphosphate synthetase I deficiency (CPS1)

 #237200

*608307

 YES

Cartilage-Hair Hypoplasia (RMRP)

#250250

*157660

 

 Cell-free fetal DNA sex determination

 

 Pending

 Connexin 26 (GJB2)

 #220290

*121011

 YES

 Crouzon syndrome (FGFR2/FGFR3)

 #123500

*176943

*134934

 NCG

 Cystic Fibrosis (CFTR)

 #219700

*602421

 

 Cystinosis (CTNS)

 #219800

#219750

#219900

*606272

 YES

 Fabry Disease (GLA)

 +301500

 YES

 Familial Hemophagocytic Lymphohistiocystosis (PRF1)

 #603553

*170280

 NCG

 Familial Hypercholesterolaemia (LDLR & APOB)

 #143890

#144010

*606945

+107730

 YES

 Fragile X syndrome (FMR1)

 +309550

 

 Gaucher disease (GBA)

 #230800

#230900

#231000

*606463

 YES

 Glycogen storage disease 1a (G6PC)

 +232200

 YES

 Glycogen storage disease type 2/Pompe disease (GAA)

 #232300

*606800

 YES

 Hypertrophic Cardiomyopathy (MYBPC3, MYH7, TNNT2, TNNI3)

 #192600

*600958

*160760

*191045

+191044

 YES

 Hypochondroplasia (FGFR3)

 #146000

*134934

 YES

 Interleukin 7 receptor severe combined immune deficiency (IL7R)

 #600802

*146661

 YES

 JAK3 severe combined immune deficiency (JAK3)

 #600802

*600173

 NCG

 Juvenile Nephronophthisis (NPHP1)

 #256100

*607100

 YES

 Krabbe disease (GALC)

 #245200

*606890

 YES

Loeys Dietz Syndrome

(TGFBR1, TGFBR2)

#610380

190181, 190182

 

 Long Chain deficiency of Acyl-CoA dehydrogenase (HADHA)

 #609016

*600890

 YES

McCune Albright Syndrome

(GNAS1)

#174800

YES

 Medium Chain deficiency of Acyl-CoA dehydrogenase (ACADM)

 #201450

*607008

 YES

 Metachromatic Leukodystrophy (ARSA)

 #250100

*607574

 YES

 Mucopolysaccharidosis type 1 (Hurler/Scheie) (IDUA)

 #607014

#607015

#607016

*252800

 YES

 Mucopolysaccharidosis type 2

(Hunter) (IDS)

 +309900

 YES

 Mucopolysaccharidosis type 3A (Sanfilippo type A) (SGSH)

 #252900

*605270

 YES

 Mucopolysaccharidosis type 3B (Sanfilippo type B) (NAGLU)

 #252920

*609701

 YES

 Muenke syndrome (FGFR3)

 #602849

*134934

 NCG

Myosin Myopathies

(MYH7)

#608358

#160500

 

 Neuronal ceroid-lipofuscinosis type 1 (infantile Batten) (CLN1, PPT1)

 #256730

*600722

 YES

 Neuronal ceroid-lipofuscinosis type 2 (late-infantile Batten) (TPP1, CLN2)

 #204500

*607998

 YES

 Neuronal ceroid-lipofuscinosis type 3 (juvenile Batten) (CLN3)

 #204200

*607042

 YES

 Neuronal ceroid-lipofuscinosis type 5 (variant late-infantile Batten) (CLN5)

 #256731

*608102

 YES

 Neuronal ceroid-lipofuscinosis type 6 (variant late-infantile Batten) (CLN6)

 #601780

*606725

 YES

 Neuronal ceroid-lipofuscinosis type 8 (variant late-infantile Batten) (CLN8)

 #600143

*607837

 YES

 Ornithine Transcarbamylase deficiency (OTC)

 #311250

*300461

 YES

 Pendred syndrome

 (SLC26A4, KCNJ10, FOXI1)

 #274600

 

 YES (SLC26A4)

 Pfeiffer syndrome (FGFR1/FGFR2)

 #101600

*136350

*176943

 NCG

 Popliteal Pterygium Syndrome (IRF6)

 #119500

*607199

 YES

 Prader Willi Syndrome

 #176270

 

 Pseudohypoparathyroidism (GNAS1)

 +139320

 YES

 Pseudo-pseudohypoparathyroidism (GNAS1)

 +139320

 YES

 Pulmonary Surfactant Metabolism Dysfunction type 1 (SFTPB)

 #265120

 YES

 Pulmonary Surfactant Metabolism Dysfunction type 2 (SFTPC)

 #610913

*178620

 YES

 Pulmonary Surfactant Metabolism Dysfunction type 3 (ABCA3)

 #610921

 *601615

 

 YES

 RAG-severe combined immune deficiency (RAG1/RAG2)

 #601457

*179615

*179616

 NCG

 Saethre-Chotzen syndrome (TWIST)

 #101400

*601622

 NCG

Silver Russell Syndrome

#180860

 

 Steroid resistant nephrotic syndrome (NPHS2)

 #600995

*604766

 YES

 Thanatophoric dysplasia (FGFR3)

 #187600

*134934

 YES

 Van der Woude syndrome (IRF6)

 #119300

*607199

 YES

Waardenburg Syndrome Type 1

(PAX3)

#193500

*606597

 

 Wiskott-Aldrich syndrome (WAS)

 #301000

*300392

 NCG

 X-inactivation studies

 

 YES

 X-linked agammaglobulinaemia (BTK)

 #307200

+300300

 YES

 X-linked Hyper IgM syndrome (CD40LG)

 #308230

*300386

 NCG

 X-linked lymphoproliferative disease (XLP1) (SH2D1A)

 #308240

*300490

 NCG

 X-linked lymphoproliferative disease (XLP2) (XIAP)

 #602450

*300079

 NCG

 X-linked Severe Combined Immune Deficiency (IL2RG)

 #300400

*308380

 NCG

Services offered outside main commissioning area geographical

boundaries under the UK specialist Genetic Testing Network - enquire to the laboratory on costs..

 NCG - nationally funded service.